Idiopathic Pulmonary Fibrosis

A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.

Also Known As:

Familial Idiopathic Pulmonary Fibrosis; Fibrocystic Pulmonary Dysplasia; Fibrosing Alveolitis, Cryptogenic; Idiopathic Fibrosing Alveolitis, Chronic Form; Idiopathic Pulmonary Fibrosis, Familial; Interstitial Pneumonitis, Usual; Pulmonary Fibrosis, Idiopathic; Usual Interstitial Pneumonia; Cryptogenic Fibrosing Alveolitides; Dysplasia, Fibrocystic Pulmonary; Fibrocystic Pulmonary Dysplasias; Fibrosing Alveolitides, Cryptogenic; Idiopathic Pulmonary Fibroses; Interstitial Pneumonia, Usual; Pneumonitides, Usual Interstitial; Pneumonitis, Usual Interstitial; Pulmonary Dysplasia, Fibrocystic; Pulmonary Fibroses, Idiopathic; Usual Interstitial Pneumonias; Usual Interstitial Pneumonitides; Usual Interstitial Pneumonitis; Cryptogenic Fibrosing Alveolitis

Respiratory Tract Diseases: 6273
- Lung Diseases: 22701
  - Interstitial Lung Diseases: 8781
    - Pulmonary Fibrosis: 8787
      - Idiopathic Pulmonary Fibrosis: 5176

Eric G Helmer Selected Research

Eric G Helmer Research Topics

Disease

Drug/Important Bio-Agent (IBA)